Scimitar syndrome: incidence, treatment, and prognosis.

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  • Additional Information
    • Subject Terms:
    • Author-Supplied Keywords:
      Airway anomaly
      Congenital heart disease
      Pulmonary veins
      Scimitar syndrome
    • Abstract:
      This study is based on a database of 16 years; we sought to define the incidence and outcome of scimitar syndrome. Of 8,771 patients, 5 (0.057%) with scimitar syndrome were identified and constituted the study population. Follow-up ranged from 1 to 16 years (median: 10 years). Diagnosis was assured by computed tomography in four patients and by cardiac catheterization in one. Two patients presented with respiratory distress soon after birth and required early pneumonectomy in one case and coil embolization of the abnormal feeding arteries to the right lower lung followed by surgical rerouting of the abnormal pulmonary vein and repair of the atrial septal defect in the other case. The former was supported by ventilator therapy for 3 years after pneumonectomy, but was finally weaned from the ventilator. Among the other three, two had repeated pneumonia that resolved after rerouting of the abnormal right pulmonary vein and cardiac repair. The asymptomatic child did not receive any intervention. In spite of the abnormal orientation of the airways, none of the four patients with detailed computed tomography imaging showed any significant compression of the airways. All five patients were doing well as of the last follow-up. In conclusion, scimitar syndrome is a very rare disease in this Asian country and the varied symptoms, such as tachypnea and repeated infection, could be improved after interventions. [ABSTRACT FROM AUTHOR]
    • :
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    • ISSN:
      0340-6199
    • DOI:
      10.1007/s00431-007-0441-z
    • Accession Number:
      28000716
  • Citations
    • ABNT:
      CHING-CHIA WANG et al. Scimitar syndrome: incidence, treatment, and prognosis. European Journal of Pediatrics, [s. l.], v. 167, n. 2, p. 155–160, 2008. Disponível em: . Acesso em: 17 ago. 2019.
    • AMA:
      Ching-Chia Wang, En-Ting Wu, Shyh-Jye Chen, et al. Scimitar syndrome: incidence, treatment, and prognosis. European Journal of Pediatrics. 2008;167(2):155-160. doi:10.1007/s00431-007-0441-z.
    • APA:
      Ching-Chia Wang, En-Ting Wu, Shyh-Jye Chen, Lu, F., Shu-Chien Huang, Jou-Kou Wang, … Mei-Hwan Wu. (2008). Scimitar syndrome: incidence, treatment, and prognosis. European Journal of Pediatrics, 167(2), 155–160. https://doi.org/10.1007/s00431-007-0441-z
    • Chicago/Turabian: Author-Date:
      Ching-Chia Wang, En-Ting Wu, Shyh-Jye Chen, Frank Lu, Shu-Chien Huang, Jou-Kou Wang, Chung-I Chang, and Mei-Hwan Wu. 2008. “Scimitar Syndrome: Incidence, Treatment, and Prognosis.” European Journal of Pediatrics 167 (2): 155–60. doi:10.1007/s00431-007-0441-z.
    • Harvard:
      Ching-Chia Wang et al. (2008) ‘Scimitar syndrome: incidence, treatment, and prognosis’, European Journal of Pediatrics, 167(2), pp. 155–160. doi: 10.1007/s00431-007-0441-z.
    • Harvard: Australian:
      Ching-Chia Wang, En-Ting Wu, Shyh-Jye Chen, Lu, F, Shu-Chien Huang, Jou-Kou Wang, Chung-I Chang & Mei-Hwan Wu 2008, ‘Scimitar syndrome: incidence, treatment, and prognosis’, European Journal of Pediatrics, vol. 167, no. 2, pp. 155–160, viewed 17 August 2019, .
    • MLA:
      Ching-Chia Wang, et al. “Scimitar Syndrome: Incidence, Treatment, and Prognosis.” European Journal of Pediatrics, vol. 167, no. 2, Feb. 2008, pp. 155–160. EBSCOhost, doi:10.1007/s00431-007-0441-z.
    • Chicago/Turabian: Humanities:
      Ching-Chia Wang, En-Ting Wu, Shyh-Jye Chen, Frank Lu, Shu-Chien Huang, Jou-Kou Wang, Chung-I Chang, and Mei-Hwan Wu. “Scimitar Syndrome: Incidence, Treatment, and Prognosis.” European Journal of Pediatrics 167, no. 2 (February 2008): 155–60. doi:10.1007/s00431-007-0441-z.
    • Vancouver/ICMJE:
      Ching-Chia Wang, En-Ting Wu, Shyh-Jye Chen, Lu F, Shu-Chien Huang, Jou-Kou Wang, et al. Scimitar syndrome: incidence, treatment, and prognosis. European Journal of Pediatrics [Internet]. 2008 Feb [cited 2019 Aug 17];167(2):155–60. Available from: http://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=c9h&AN=28000716