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Academic Journal

A Novel SCA3 Knock-in Mouse Model Mimics the Human SCA3 Disease Phenotype Including Neuropathological, Behavioral, and Transcriptional Abnormalities Especially in Oligodendrocytes.

  • Authors : Haas E; Institute of Medical Genetics and Applied Genomics, University of Tübingen, Tübingen, Germany.; Centre for Rare Diseases, University of Tübingen, Tübingen, Germany.

Subjects: Disease Models, Animal* ; Phenotype*; Ataxin-3/Ataxin-3/Ataxin-3/*genetics

  • Source: Molecular neurobiology [Mol Neurobiol] 2022 Jan; Vol. 59 (1), pp. 495-522. Date of Electronic Publication: 2021 Oct 30.Publisher: Humana Press Country of Publication: United States NLM ID: 8900963 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Overexpression of Mutant Ataxin-3 in Mouse Cerebellum Induces Ataxia and Cerebellar Neuropathology.

Subjects: NEURODEGENERATION; GENE expression; MJD1 protein

  • Source: Cerebellum; Aug2013, Vol. 12 Issue 4, p441-455, 15p

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Academic Journal

Silencing Mutant Ataxin-3 Rescues Motor Deficits and Neuropathology in Machado-Joseph Disease Transgenic Mice.

Subjects: SPINOCEREBELLAR ataxia; GENETIC code; GENES

  • Source: PLoS ONE; Jan2013, Vol. 8 Issue 1, Special section p1-11, 11p

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Academic Journal

Graft-derived neurons and bystander effects are maintained for six months after human iPSC-derived NESC transplantation in mice's cerebella.

Subjects: RADIATION-induced bystander effect; NEURONS; CEREBELLUM

  • Source: Scientific Reports; 2/8/2024, Vol. 14 Issue 1, p1-20, 20p

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Academic Journal

Growth hormone rescue cerebellar degeneration in SCA3 transgenic mice.

  • Authors : Wu S; Department of Neurology, Changhua Christian Hospital, Changhua, Taiwan.; Liu K

Subjects: Cerebellum/Cerebellum/Cerebellum/*drug effects ; Growth Hormone/Growth Hormone/Growth Hormone/*therapeutic use ; Machado-Joseph Disease/Machado-Joseph Disease/Machado-Joseph Disease/*drug therapy

  • Source: Biochemical and biophysical research communications [Biochem Biophys Res Commun] 2020 Aug 20; Vol. 529 (2), pp. 467-473. Date of Electronic Publication: 2020 Jul 02.Publisher: Elsevier Country of Publication: United States NLM ID: 0372516 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Protective roles of carbonic anhydrase 8 in Machado-Joseph Disease.

  • Authors : Hsieh M; Department of Life Science, Tunghai University, Taichung, Taiwan, Republic of China.; Life Science Research Center, Tunghai University, Taichung, Taiwan, Republic of China.

Subjects: Biomarkers, Tumor/Biomarkers, Tumor/Biomarkers, Tumor/*metabolism ; Carbonic Anhydrases/Carbonic Anhydrases/Carbonic Anhydrases/*metabolism ; Cerebellum/Cerebellum/Cerebellum/*metabolism

  • Source: Journal of neuroscience research [J Neurosci Res] 2019 Oct; Vol. 97 (10), pp. 1278-1297. Date of Electronic Publication: 2019 Jun 03.Publisher: Wiley Interscience Country of Publication: United States NLM ID: 7600111 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Cerebellar contribution to the cognitive alterations in SCA1: evidence from mouse models.

Subjects: Ataxin-1/Ataxin-1/Ataxin-1/*metabolism ; Cerebellum/Cerebellum/Cerebellum/*metabolism ; Cognitive Dysfunction/Cognitive Dysfunction/Cognitive Dysfunction/*metabolism

  • Source: Human molecular genetics [Hum Mol Genet] 2020 Jan 01; Vol. 29 (1), pp. 117-131.Publisher: IRL Press at Oxford University Press Country of Publication: England NLM ID: 9208958 Publication Model: Print Cited Medium: Internet ISSN:

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Academic Journal

Far-infrared Radiation Improves Motor Dysfunction and Neuropathology in Spinocerebellar Ataxia Type 3 Mice.

  • Authors : Liu SW; Vascular and Genomic Center, Changhua Christian Hospital, 135 Nanhsiao Street, Changhua, 50094, Taiwan.; Chang JC

Subjects: Motor Activity*/Motor Activity*/Motor Activity*/radiation effects; Cerebellum/Cerebellum/Cerebellum/*pathology ; Infrared Rays/Infrared Rays/Infrared Rays/*therapeutic use

  • Source: Cerebellum (London, England) [Cerebellum] 2019 Feb; Vol. 18 (1), pp. 22-32.Publisher: Springer Country of Publication: United States NLM ID: 101089443 Publication Model: Print Cited Medium: Internet ISSN: 1473-4230

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Academic Journal

Mutant ataxin-3 with an abnormally expanded polyglutamine chain disrupts dendritic development and metabotropic glutamate receptor signaling in mouse cerebellar Purkinje cells.

  • Authors : Konno A; Department of Neurophysiology, Gunma University Graduate School of Medicine, Maebashi, Gunma, 371-8511, Japan.; Shuvaev AN

Subjects: Cerebellum/Cerebellum/Cerebellum/*physiology ; Dendrites/Dendrites/Dendrites/*physiology ; Nuclear Proteins/Nuclear Proteins/Nuclear Proteins/*metabolism

  • Source: Cerebellum (London, England) [Cerebellum] 2014 Feb; Vol. 13 (1), pp. 29-41.Publisher: Springer Country of Publication: United States NLM ID: 101089443 Publication Model: Print Cited Medium: Internet ISSN: 1473-4230

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Academic Journal

Cerebellar soluble mutant ataxin-3 level decreases during disease progression in Spinocerebellar Ataxia Type 3 mice.

  • Authors : Nguyen HP; Institute of Medical Genetics and Applied Genomics, University of Tuebingen, Tuebingen, Germany.; Hübener J

Subjects: Cerebellum/Cerebellum/Cerebellum/*metabolism ; Machado-Joseph Disease/Machado-Joseph Disease/Machado-Joseph Disease/*metabolism ; Nuclear Proteins/Nuclear Proteins/Nuclear Proteins/*metabolism

  • Source: PloS one [PLoS One] 2013 Apr 23; Vol. 8 (4), pp. e62043. Date of Electronic Publication: 2013 Apr 23 (Print Publication: 2013).Publisher: Public Library of Science Country of Publication: United States NLM ID: 101285081 Publication Model: Electronic-Print Cited Medium: Internet

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  • 1-10 of  93 results for ""Ataxin-3""