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Academic Journal

Understanding CFTR Functionality: A Comprehensive Review of Tests and Modulator Therapy in Cystic Fibrosis.

  • Authors : Thakur S; School of Pharmaceutical Sciences, Lovely Professional University, Phagwara, Panjab, India.; Ankita

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics; Humans

  • Source: Cell biochemistry and biophysics [Cell Biochem Biophys] 2024 Mar; Vol. 82 (1), pp. 15-34. Date of Electronic Publication: 2023 Dec 04.Publisher: Humana Press Country of Publication: United States NLM ID: 9701934 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Nanoparticle-based platforms for targeted drug delivery to the pulmonary system as therapeutics to curb cystic fibrosis: A review.

  • Authors : Rano S; Department of Biotechnology, Haldia Institute of Technology, HIT Campus, Purba Medinipur, Haldia 721657, West Bengal, India; In-vitro Biology, Aragen Life Sciences, Hyderabad 500076, Telangana, India.

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/microbiology ; Nanoparticles*

  • Source: Journal of microbiological methods [J Microbiol Methods] 2024 Feb-Mar; Vol. 217-218, pp. 106876. Date of Electronic Publication: 2023 Dec 20.Publisher: Elsevier Biomedical Country of Publication: Netherlands NLM ID: 8306883 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Report

Use of CFTR Modulators for Cystic Fibrosis in a Patient with Liver Transplant and ESRD on Hemodialysis.

  • Authors : Hu L; UO Nefrologia, Dialisi e Trapianto - IRCCS Azienda Ospedaliero-Universitaria di Bologna, Bologna, Italia.; Bruno PF

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/complications ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics

  • Source: Giornale italiano di nefrologia : organo ufficiale della Societa italiana di nefrologia [G Ital Nefrol] 2024 Feb 28; Vol. 41 (1). Date of Electronic Publication: 2024 Feb 28.Publisher: Società Italiana di Nefrologia Country of Publication: Italy NLM ID: 9426434 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Sex differences in outcomes of people with cystic fibrosis treated with elexacaftor/tezacaftor/ivacaftor.

  • Authors : Wang A; School of Medicine, University of Texas Southwestern Medical Center, Dallas, TX, USA.; Lee M

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/diagnosis ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/epidemiology

  • Source: Journal of cystic fibrosis : official journal of the European Cystic Publisher: Elsevier Country of Publication: Netherlands NLM ID: 101128966 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Severe lung disease in children with cystic fibrosis missed in newborn screening.

  • Authors : Baldwin K; Department of Pediatrics, Rutgers Robert Wood Johnson Medical School, New Brunswick, New Jersey, USA.; Barker EM

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/complications ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/diagnosis ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics

  • Source: Pediatric pulmonology [Pediatr Pulmonol] 2024 Jan; Vol. 59 (1), pp. 163-168. Date of Electronic Publication: 2023 Oct 27.Publisher: Wiley-Liss Country of Publication: United States NLM ID: 8510590 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

A longitudinal analysis of respiratory symptoms in people with cystic fibrosis with advanced lung disease on and off ETI.

  • Authors : Gill ER; Division of Biobehavioral Nursing and Health Informatics, Dept of Nursing, University of Washington, Seattle WA, USA.; Bartlett LE

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/complications ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Pyrrolidines*

  • Source: Journal of cystic fibrosis : official journal of the European Cystic Publisher: Elsevier Country of Publication: Netherlands NLM ID: 101128966 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Effect of CFTR modulator therapy with elexacaftor/tezacaftor/ivacaftor on pulmonary ventilation derived by 3D phase-resolved functional lung MRI in cystic fibrosis patients.

  • Authors : Klimeš F; Institute of Diagnostic and Interventional Radiology, Hannover Medical School, Hannover, Germany.; Biomedical Research in Endstage and Obstructive Lung Disease Hannover (BREATH), German Center for Lung Research (DZL), Hannover, Germany.

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/diagnostic imaging ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Benzodioxoles*

  • Source: European radiology [Eur Radiol] 2024 Jan; Vol. 34 (1), pp. 80-89. Date of Electronic Publication: 2023 Aug 07.Publisher: Springer International Country of Publication: Germany NLM ID: 9114774 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Rate and predictors of insufficient sweat volume in very young infants after pilocarpine gel iontophoresis: prospective, population-based study.

  • Authors : Camargos P; Department of Pediatrics, Universidade Federal de Minas Gerais, Belo Horizonte, Brazil .; Bedran RM

Subjects: Pilocarpine* ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/diagnosis ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/epidemiology

  • Source: Archives of disease in childhood [Arch Dis Child] 2024 Mar 19; Vol. 109 (4), pp. 304-307. Date of Electronic Publication: 2024 Mar 19.Publisher: BMJ Pub. Group [etc.] Country of Publication: England NLM ID: 0372434 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Outcome data from 15 years of cystic fibrosis newborn screening in a large UK region.

  • Authors : Driscoll SJ; Staffordshire Children's Hospital at Royal Stoke, University Hospital of North Staffordshire NHS Trust, Stoke on Trent, UK.; Heinz K

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/diagnosis ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/epidemiology ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics

  • Source: Archives of disease in childhood [Arch Dis Child] 2024 Mar 19; Vol. 109 (4), pp. 292-296. Date of Electronic Publication: 2024 Mar 19.Publisher: BMJ Pub. Group [etc.] Country of Publication: England NLM ID: 0372434 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

A novel high-resolution melting analysis strategy for detecting cystic fibrosis-causing variants.

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/diagnosis ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics; Infant, Newborn

  • Source: Laboratory medicine [Lab Med] 2024 Mar 07; Vol. 55 (2), pp. 185-197.Publisher: Oxford University Press Country of Publication: England NLM ID: 0250641 Publication Model: Print Cited Medium: Internet ISSN:

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  • 1-10 of  136,912 results for ""CYSTIC fibrosis""