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Academic Journal

Understanding CFTR Functionality: A Comprehensive Review of Tests and Modulator Therapy in Cystic Fibrosis.

  • Authors : Thakur S; School of Pharmaceutical Sciences, Lovely Professional University, Phagwara, Panjab, India.; Ankita

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics; Humans

  • Source: Cell biochemistry and biophysics [Cell Biochem Biophys] 2024 Mar; Vol. 82 (1), pp. 15-34. Date of Electronic Publication: 2023 Dec 04.Publisher: Humana Press Country of Publication: United States NLM ID: 9701934 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Cystic fibrosis and fat malabsorption: Pathophysiology of the cystic fibrosis gastrointestinal tract and the impact of highly effective CFTR modulator therapy.

  • Authors : McDonald CM; Cystic Fibrosis Center, Primary Children's Hospital, Salt Lake City, Utah, USA.; Reid EK

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/complications ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Malabsorption Syndromes*/Malabsorption Syndromes*/Malabsorption Syndromes*/complications

  • Source: Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition [Nutr Clin Pract] 2024 Apr; Vol. 39 Suppl 1, pp. S57-S77.Publisher: Wiley Country of Publication: United States NLM ID: 8606733 Publication Model: Print Cited Medium: Internet ISSN: 1941-2452

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Academic Journal

Gilbert's syndrome leads to elevated bilirubin after initiation of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis.

  • Authors : Patel N; Division of Pulmonary Disease, Critical Care and Sleep Medicine, University of Kansas Medical Center, Kansas City, Kansas, USA.; Ansar M

Subjects: Gilbert Disease* ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/complications ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy

  • Source: Pediatric pulmonology [Pediatr Pulmonol] 2024 Apr; Vol. 59 (4), pp. 863-866. Date of Electronic Publication: 2024 Jan 05.Publisher: Wiley-Liss Country of Publication: United States NLM ID: 8510590 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Lumacaftor/Ivacaftor Population Pharmacokinetics in Pediatric Patients with Cystic Fibrosis: A First Step Toward Personalized Therapy.

  • Authors : Bouazza N; Université Paris Cité, EA7323, Paris, France. .; Unité de Recherche Clinique Necker Cochin, AP-HP, Paris, France. .

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics ; Quinolones*

  • Source: Clinical pharmacokinetics [Clin Pharmacokinet] 2024 Mar; Vol. 63 (3), pp. 333-342. Date of Electronic Publication: 2024 Feb 04.Publisher: Country of Publication: Switzerland NLM ID: 7606849 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1179-1926

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Academic Journal

Analysis of iron status after initiation of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis.

  • Authors : James A; Department of Medicine, University of Virginia School of Medicine, Charlottesville, Virginia, USA.; Li G

Subjects: Iron* ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/complications ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy

  • Source: Pediatric pulmonology [Pediatr Pulmonol] 2024 Mar; Vol. 59 (3), pp. 669-678. Date of Electronic Publication: 2023 Dec 13.Publisher: Wiley-Liss Country of Publication: United States NLM ID: 8510590 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Editorial & Opinion

Body composition in children with cystic fibrosis treated with CFTR modulators versus modulator naïve individuals.

  • Authors : Dress C; Division of Pulmonary Medicine , Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.; Hente E

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics; Child

  • Source: Pediatric pulmonology [Pediatr Pulmonol] 2024 Mar; Vol. 59 (3), pp. 805-808. Date of Electronic Publication: 2023 Dec 20.Publisher: Wiley-Liss Country of Publication: United States NLM ID: 8510590 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Risk of CFTR-related disorders and cystic fibrosis in an Italian cohort of CRMS/CFSPID subjects in preschool and school age.

  • Authors : Fevola C; Department of Pediatric Medicine, Meyer Children's Hospital IRCCS, Cystic Fibrosis Regional Reference Center, Viale Gaetano Pieraccini 2, Florence, 50139, Italy.; Dolce D

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/diagnosis ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics; Infant

  • Source: European journal of pediatrics [Eur J Pediatr] 2024 Feb; Vol. 183 (2), pp. 929-938. Date of Electronic Publication: 2023 Dec 06.Publisher: Springer Verlag Country of Publication: Germany NLM ID: 7603873 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Nanoparticle-based platforms for targeted drug delivery to the pulmonary system as therapeutics to curb cystic fibrosis: A review.

  • Authors : Rano S; Department of Biotechnology, Haldia Institute of Technology, HIT Campus, Purba Medinipur, Haldia 721657, West Bengal, India; In-vitro Biology, Aragen Life Sciences, Hyderabad 500076, Telangana, India.

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/drug therapy ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/microbiology ; Nanoparticles*

  • Source: Journal of microbiological methods [J Microbiol Methods] 2024 Feb-Mar; Vol. 217-218, pp. 106876. Date of Electronic Publication: 2023 Dec 20.Publisher: Elsevier Biomedical Country of Publication: Netherlands NLM ID: 8306883 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Time to be blunt: Substance use in cystic fibrosis.

  • Authors : Vaziri S; Department of Pediatrics, University of California San Francisco, San Francisco, California, USA.; McGarry ME

Subjects: Electronic Nicotine Delivery Systems* ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/epidemiology ; Substance-Related Disorders*/Substance-Related Disorders*/Substance-Related Disorders*/epidemiology

  • Source: Pediatric pulmonology [Pediatr Pulmonol] 2024 Apr; Vol. 59 (4), pp. 1015-1027. Date of Electronic Publication: 2024 Jan 22.Publisher: Wiley-Liss Country of Publication: United States NLM ID: 8510590 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

[Therapeutics in cystic fibrosis: Clinical revolution and new challenges].

  • Authors : Bardin E; Université Paris Cité, Inserm U1151, Institut Necker Enfants Malades, Paris, France.; Pranke I

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/genetics ; Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/therapy; Humans

  • Source: Medecine sciences : M/S [Med Sci (Paris)] 2024 Mar; Vol. 40 (3), pp. 258-267. Date of Electronic Publication: 2024 Mar 22.Publisher: EDK Country of Publication: France NLM ID: 8710980 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1958-5381

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  • 1-10 of  893,608 results for ""Cystic Fibrosis""