Search Results

Recessively Inherited Deficiency of Secreted WFDC2 (HE4) Causes Nasal Polyposis and Bronchiectasis.

• Authors : Dougherty GW; University Children's Hospital Muenster, Muenster, Germany.; Ostrowski LE

• Source: American journal of respiratory and critical care medicine [Am J Respir Crit Care Med] 2024 Apr 16. Date of Electronic Publication: 2024 Apr 16.Publisher: American Thoracic Society Country of Publication: United States NLM ID: 9421642 Publication Model: Print-Electronic Cited Medium: Internet

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Bronchiectasis-associated infections and outcomes in a large, geographically diverse electronic health record cohort in the United States.

• Authors : Dean SG; Epidemiology and Population Studies Unit, Division of Intramural Research, National Institute of Allergy and Infectious Diseases, National Institutes of Health , Bethesda, USA.; Blakney RA

Subjects: Bronchiectasis*/Bronchiectasis*/Bronchiectasis*/epidemiology ; Bronchiectasis*/Bronchiectasis*/Bronchiectasis*/complications ; Pseudomonas Infections*/Pseudomonas Infections*/Pseudomonas Infections*/drug therapy

• Source: BMC pulmonary medicine [BMC Pulm Med] 2024 Apr 10; Vol. 24 (1), pp. 172. Date of Electronic Publication: 2024 Apr 10.Publisher: BioMed Central Country of Publication: England NLM ID: 100968563 Publication Model: Electronic Cited Medium: Internet ISSN: 1471-2466

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Proximal and Distal Bronchioles Contribute to the Pathogenesis of Non-Cystic Fibrosis Bronchiectasis.

• Authors : Asakura T; Marsico Lung Institute/Cystic Fibrosis Research Center.; Department of Clinical Medicine, Laboratory of Bioregulatory Medicine, Kitasato University School of Pharmacy, Tokyo, Japan.

Subjects: Bronchiectasis*/Bronchiectasis*/Bronchiectasis*/genetics ; Cystic Fibrosis*; Humans

• Source: American journal of respiratory and critical care medicine [Am J Respir Crit Care Med] 2024 Feb 15; Vol. 209 (4), pp. 374-389.Publisher: American Thoracic Society Country of Publication: United States NLM ID: 9421642 Publication Model: Print Cited Medium: Internet ISSN:

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Airway inflammation accelerates pulmonary exacerbations in cystic fibrosis.

• Authors : Liou TG; Adult Cystic Fibrosis Center, Division of Respiratory, Critical Care and Occupational Pulmonary Medicine, Department of Internal Medicine, University of Utah, 26 North Mario Capecchi Drive, Salt Lake City, UT 84132, USA.; Primary Children's Cystic Fibrosis Center, Division of Pediatric Pulmonology, Department of Pediatrics, University of Utah, 81 North Mario Capecchi Drive, Salt Lake City, UT 84113, USA.

• Source: IScience [iScience] 2024 Jan 09; Vol. 27 (3), pp. 108835. Date of Electronic Publication: 2024 Jan 09 (Print Publication: 2024).Publisher: Cell Press Country of Publication: United States NLM ID: 101724038 Publication Model: eCollection Cited Medium: Internet ISSN:

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Situs Ambiguus Is Associated With Adverse Clinical Outcomes in Children With Primary Ciliary Dyskinesia.

• Authors : Kaspy KR; McGill University Health Centre Research Institute, Montreal Children's Hospital, Montreal, QC.; Dell SD

• Source: Chest [Chest] 2023 Dec 09. Date of Electronic Publication: 2023 Dec 09.Publisher: Elsevier Country of Publication: United States NLM ID: 0231335 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Host-Directed Therapy in Nontuberculous Mycobacterial Pulmonary Disease: Preclinical and Clinical Data Review.

• Authors : Anidi IU; Pulmonary Division, National Heart, Lung and Blood Institute, National Institutes of Health, 33 North Drive, Room 1W10A, Bethesda, MD 20892, USA. Electronic address: .; Olivier KN

Subjects: Mycobacterium Infections, Nontuberculous*/Mycobacterium Infections, Nontuberculous*/Mycobacterium Infections, Nontuberculous*/drug therapy ; Mycobacterium Infections, Nontuberculous*/Mycobacterium Infections, Nontuberculous*/Mycobacterium Infections, Nontuberculous*/microbiology ; Lung Diseases*/Lung Diseases*/Lung Diseases*/drug therapy

• Source: Clinics in chest medicine [Clin Chest Med] 2023 Dec; Vol. 44 (4), pp. 839-845. Date of Electronic Publication: 2023 Aug 23.Publisher: Elsevier Health Sciences Division Country of Publication: United States NLM ID: 7907612 Publication Model: Print-Electronic Cited Medium:

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Evolution of Mycobacterium abscessus in the human lung: Cumulative mutations and genomic rearrangement of porin genes in patient isolates.

• Authors : Shallom SJ; Microbiology Service, Department of Laboratory Medicine (DLM), Clinical Center, NIH, Bethesda, MD, USA.; Tettelin H

Subjects: Cystic Fibrosis*/Cystic Fibrosis*/Cystic Fibrosis*/microbiology ; Mycobacterium*/Mycobacterium*/Mycobacterium*/genetics ; Mycobacterium abscessus*/Mycobacterium abscessus*/Mycobacterium abscessus*/genetics

• Source: Virulence [Virulence] 2023 Dec; Vol. 14 (1), pp. 2215602.Publisher: Taylor & Francis Country of Publication: United States NLM ID: 101531386 Publication Model: Print Cited Medium: Internet ISSN:

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Long-term Safety and Tolerability of Omadacycline for the Treatment of Mycobacterium abscessus Infections.

• Authors : Mingora CM; Medical University of South Carolina, Charleston, South Carolina, USA.; Bullington W

• Source: Open forum infectious diseases [Open Forum Infect Dis] 2023 Jul 03; Vol. 10 (7), pp. ofad335. Date of Electronic Publication: 2023 Jul 03 (Print Publication: 2023).Publisher: Published by Oxford University Press on behalf of the Infectious Diseases Society of America Country of Publication: United States NLM ID: 101637045

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Chromosomal microarray analysis supplements exome sequencing to diagnose children with suspected inborn errors of immunity.

• Authors : Beers BJ; National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, United States.; Similuk MN

Subjects: Chromosomes* ; Genetic Testing*; Humans

• Source: Frontiers in immunology [Front Immunol] 2023 May 05; Vol. 14, pp. 1172004. Date of Electronic Publication: 2023 May 05 (Print Publication: 2023).Publisher: Frontiers Research Foundation] Country of Publication: Switzerland NLM ID: 101560960 Publication Model: eCollection Cited Medium: Internet

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Laterality Defects in Primary Ciliary Dyskinesia: Relationship to Ultrastructural Defect or Genotype.

• Authors : Barber AT; Department of Pediatrics, UNC Children's, and.; Shapiro AJ

Subjects: Heterotaxy Syndrome* ; Ciliary Motility Disorders* ; Kartagener Syndrome*/Kartagener Syndrome*/Kartagener Syndrome*/genetics

• Source: Annals of the American Thoracic Society [Ann Am Thorac Soc] 2023 Mar; Vol. 20 (3), pp. 397-405.Publisher: American Thoracic Society Country of Publication: United States NLM ID: 101600811 Publication Model: Print Cited Medium: Internet ISSN:

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